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Congenital Bleeding Disorders = Dia...
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Dorgalaleh, Akbar.
Congenital Bleeding Disorders = Diagnosis and Management /
紀錄類型:
書目-語言資料,印刷品 : Monograph/item
正題名/作者:
Congenital Bleeding Disorders / edited by Akbar Dorgalaleh.
其他題名:
Diagnosis and Management /
其他作者:
Dorgalaleh, Akbar.
面頁冊數:
XIV, 396 p. 93 illus., 85 illus. in color.online resource. :
Contained By:
Springer Nature eBook
標題:
Hematology. -
電子資源:
https://doi.org/10.1007/978-3-319-76723-9
ISBN:
9783319767239
Congenital Bleeding Disorders = Diagnosis and Management /
Congenital Bleeding Disorders
Diagnosis and Management /[electronic resource] :edited by Akbar Dorgalaleh. - 1st ed. 2018. - XIV, 396 p. 93 illus., 85 illus. in color.online resource.
Part I: Common bleeding disorders -- 1. Von Willebrand disease -- 2. Hemophilia A (congenital factor VIII deficiency) -- 3. Hemophilia B (congenital factor IX deficiency) Part II: Rare bleeding disorders -- 4. Congenital factor I (fibrinogen) disorders -- 5. Congenital factor II deficiency -- 6. Congenital factor V deficiency -- 7. Combined coagulation factor deficiencies -- 8. Congenital factor VII deficiency -- 9. Congenital factor X deficiency -- 10. Congenital factor XI deficiency -- 11. Congenital factor XIII deficiency Part III: Inherited platelet function disorders -- 12. Glanzmann thrombasthenia -- 13. Bernard–Soulier syndrome -- 14. Gray platelet syndrome -- 15. Quebec platelet disorder. .
This book describes in detail the clinical presentation, diagnosis, and management of a wide range of congenital bleeding disorders. It will assist readers in overcoming the significant challenges involved in clinical and laboratory diagnosis and in providing effective clinical care that makes optimal use of new products, including recombinant factor concentrate. The coverage ranges from hemophilia A and B and von Willebrand disease to rare bleeding disorders such as congenital factor V, factor X, factor XI, and factor XIII deficiency and inherited platelet function disorders. The exceptional attention to rarer conditions is of particular importance given the considerable risk of overlooking them during diagnosis, with potential consequences for disease-related morbidity and mortality. The authors are acknowledged specialists in the field from across the world who have particular expertise in the disorder that they discuss. The book will be of value to hematologists, oncologists, pediatricians, laboratory specialists and technicians, general physicians, and trainees. .
ISBN: 9783319767239
Standard No.: 10.1007/978-3-319-76723-9doiSubjects--Topical Terms:
645254
Hematology.
LC Class. No.: RB45
Dewey Class. No.: 616.15
Congenital Bleeding Disorders = Diagnosis and Management /
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Part I: Common bleeding disorders -- 1. Von Willebrand disease -- 2. Hemophilia A (congenital factor VIII deficiency) -- 3. Hemophilia B (congenital factor IX deficiency) Part II: Rare bleeding disorders -- 4. Congenital factor I (fibrinogen) disorders -- 5. Congenital factor II deficiency -- 6. Congenital factor V deficiency -- 7. Combined coagulation factor deficiencies -- 8. Congenital factor VII deficiency -- 9. Congenital factor X deficiency -- 10. Congenital factor XI deficiency -- 11. Congenital factor XIII deficiency Part III: Inherited platelet function disorders -- 12. Glanzmann thrombasthenia -- 13. Bernard–Soulier syndrome -- 14. Gray platelet syndrome -- 15. Quebec platelet disorder. .
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This book describes in detail the clinical presentation, diagnosis, and management of a wide range of congenital bleeding disorders. It will assist readers in overcoming the significant challenges involved in clinical and laboratory diagnosis and in providing effective clinical care that makes optimal use of new products, including recombinant factor concentrate. The coverage ranges from hemophilia A and B and von Willebrand disease to rare bleeding disorders such as congenital factor V, factor X, factor XI, and factor XIII deficiency and inherited platelet function disorders. The exceptional attention to rarer conditions is of particular importance given the considerable risk of overlooking them during diagnosis, with potential consequences for disease-related morbidity and mortality. The authors are acknowledged specialists in the field from across the world who have particular expertise in the disorder that they discuss. The book will be of value to hematologists, oncologists, pediatricians, laboratory specialists and technicians, general physicians, and trainees. .
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